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CYSTADANE (BETAINE)
- Homocystinuria
1 gram/1.7 mL oral powder
- 3 scoops (3 gram) by oral route 2 times per day
Homocystinuria
- 3 scoops (3 gram) by oral route 2 times per day
- None
Contraindicated
- None
Severe
Moderate
- None
- None
Contraindicated
- Cerebral edema
- Hypermethioninemia
Severe
Moderate
- None
CYSTADANE (BETAINE)
- Homocystinuria
- None
- Gastrointestinal irritation
- Nausea
More Frequent
Severe
Less Severe
- None
- Body odor
- Dysgeusia
- Dyspepsia
Less Frequent
Severe
Less Severe
Rare / Very Rare
Severe
- Cerebral edema
- Hypermethioninemia
Less Severe
- Agitation
- Alopecia
- Anorexia
- Depression
- Diarrhea
- Glossitis
- Irritability
- Personality disorders
- Sleep disorder
- Tooth disorder
- Urinary incontinence
- Urticaria
- Vomiting
Contraindicated
None
Severe Precaution
None
Management or Monitoring Precaution
Betaine
Start at lower dose (100mg/kg/day divided) and titrate.
- 1 Day – 3 Years
- Start at lower dose (100mg/kg/day divided) and titrate.
Betaine
- Severity Level:
2
- Additional Notes: Limited human data do not suggest a clear association for development toxicity.
Contraindicated
None
General | Excretion Potential | Effect on Infant | Notes |
None |
Precaution Exists
Betaine
No data available.
General | Excretion Potential | Effect on Infant | Notes |
Evaluate use carefully | Unknown | Not known; no or inclusive data | No data available. |
No Known Risk
None
General | Excretion Potential | Effect on Infant | Notes |
None |
Contraindicated
None
Precaution Exists
None
No Known Risk
None
- None
Homocystinuria | |
E72.11 | Homocystinuria |
0-9 | A-Z |
---|---|
E72.11 | Homocystinuria |
Formulary Reference Tool